What is the appropriate duration of treatment for emphysematous cystitis? Is there any evidence to support shorter courses of therapy?

Comment by InpharmD Researcher

There is no recommendation regarding the length of antibiotic treatment for emphysematous cystitis, as treatment must be individualized based on susceptibility patterns and the duration primarily depends on patient response (i.e., decreased gas accumulation). In general, antibiotics are administered until improvements are observed, which could range from 7-10 days or beyond, and could be followed with a prolonged course of oral antibiotics for multiple weeks.

Background

A 2014 review discusses the treatment of emphysematous cystitis. Most cases are generally initiated with an initial IV antibiotic, tailored accordingly to the results of the culture. The duration of treatment is not specified, but usually continues until clinical improvement is observed. From there, treatment can continue or patients may switch to oral therapy. There is no discussion regarding repeat imaging beyond the diagnostic period. [1]

According to a 2007 review of 135 cases, the treatment course with antibiotics generally depends on the sensitivity of the urinary pathogen. While not directly stated, the author’s discussion suggests that antibiotics should continue until patients show improvement and response. Imaging, with plain films or computed tomography, are the standard means for diagnosis. But the benefits of repeat imaging to confirm treatment is not discussed. While conservative management is advocated for limiting cases, it remains poorly defined, suggesting an individualized approach per patient. [2]

Several case reports (See Tables 1-4) described experience in treating emphysematous cystitis, although with limited information specific to length of treatment. A 2023 case report detailed the successful conservative management of emphysematous cystitis with pneumoperitoneum in a 90-year-old woman. The patient, initially hospitalized for a hemorrhagic gastric ulcer, developed acute lower abdominal pain and hematuria six days into admission. Contrast-enhanced CT imaging revealed gas within the bladder wall, diagnostic of emphysematous cystitis, alongside pneumoperitoneum. Despite the presence of free air in the abdomen, no definitive signs of bladder or gastrointestinal perforation were evident on imaging. Given the patient's advanced age and frailty, conservative management was prioritized over surgical exploration. A urethral catheter was placed, and empirical intravenous meropenem was initiated for approximately 6 days, later de-escalated to ceftriaxone for an additional two weeks upon identification of Klebsiella pneumoniae in the urine culture. The patient demonstrated clinical improvement, and repeat imaging on day 18 confirmed the resolution of emphysematous changes and pneumoperitoneum, leading to hospital discharge on day 40. The findings suggest that patients can be managed through conservative treatment. [3]

Additionally, a 2013 case report detailed the successful management of a rare emphysematous cyst infection in a 62-year-old female patient with a 15-year history of autosomal dominant polycystic kidney disease (ADPKD). The patient presented with intermittent fever, nausea, and left flank discomfort, and imaging via CT, which demonstrated an 8.1 cm gas-forming, infected renal cyst in the left kidney. Escherichia coli was identified as the causative organism through cyst fluid culture. Despite initial management with intravenous ciprofloxacin for one week at an outside facility, the patient showed no significant improvement in symptoms or clinical parameters, prompting her referral for further intervention. Laboratory findings on presentation included elevated white blood cell counts (12,850/mcL) and C-reactive protein (6.79 mg/dL), alongside notable abnormalities in urinalysis. The treatment involved a combination of intravenous ciprofloxacin at 400 mg daily and percutaneous cystostomy drainage with intracystic ciprofloxacin irrigation. The intracystic therapy consisted of 100 mg of ciprofloxacin diluted in 450 mL of normal saline, delivered over six days. This novel approach led to significant clinical improvement, with resolution of generalized weakness, nausea, and flank discomfort, accompanied by normalization of inflammatory markers. Follow-up CT imaging revealed a reduction in the size of the infected cyst from 8.1 cm to 4.7 cm with decreased internal air attenuation. The patient was discharged on oral ciprofloxacin for six additional weeks, and no surgical intervention, such as nephrectomy, was required. This report highlights the potential efficacy of combining systemic and localized antibiotic therapies for treating emphysematous cyst infections in ADPKD patients, particularly those contraindicated for surgery. [4]

A 2009 case report detailed an 89-year-old woman diagnosed with emphysematous cystitis despite lacking typical predisposing factors such as diabetes or immunosuppression. The patient presented following a mechanical fall but exhibited mild abdominal discomfort and suprapubic tenderness. Laboratory findings revealed leukocytosis with a white blood cell count of 19.5 × 10⁹/L, pyuria, and bacteriuria, but urine cultures taken post-antibiotic initiation were negative. Imaging studies, including a plain abdominal X-ray and computed tomography (CT), identified gas within the bladder wall, confirming the diagnosis. Initial intravenous (IV) ciprofloxacin therapy was discontinued due to delirium, and the patient was switched to aztreonam, completing a 7-day course. She demonstrated clinical improvement, marked by resolution of symptoms and a subsequent decrease in leukocytosis. A follow-up abdominal X-ray one-month post-discharge confirmed the resolution of emphysematous cystitis. A literature review in the same publication analyzed 15 previously reported cases of emphysematous cystitis in immunocompetent, nondiabetic patients from 1970 to 2009, identifying advanced age as a common characteristic. The majority of cases involved females, with abdominal pain being the most frequently reported symptom. Escherichia coli was the predominant pathogen, isolated in 70% of cases where culture data was available. Imaging studies were crucial for diagnosis, as clinical manifestations varied, and only half of the reported cases exhibited classic urinary symptoms. Treatment primarily involved antimicrobial therapy (e.g., gentamicin and piperacillin/tazobactam then cefuroxime; liposomal amphotericin B and 5-flucytosin; piperacillin then ceftazidime; ​​cefotiam; cefazolin, gentamicin, and metronidazole then oral ofloxacin and metronidazole) often in conjunction with bladder catheterization, with a standard duration of 7–10 days. Although the prognosis was generally favorable, one patient succumbed to the infection. The findings underscored the necessity for heightened clinical suspicion and prompt imaging in elderly patients presenting with atypical urinary symptoms, even in the absence of traditional risk factors. [5]

Finally, another 2024 case report details the presentation and management of a 70-year-old woman diagnosed with severe emphysematous cystitis. The patient, with a history of diabetes and active chemotherapy for breast cancer, exhibited profound asthenia and pain in the right lower extremity without fever or urinary symptoms. Cross-sectional imaging through CT identified extensive gas accumulation within the bladder wall, confirming the presence of emphysematous cystitis. Given the patient’s immunocompromised status, an empiric antimicrobial regimen was initiated alongside bladder catheterization, aiming to resolve the infection while preventing complications. Serial imaging demonstrated a marked reduction in intramural gas, suggesting clinical improvement with conservative treatment. A therapeutic course of IV piperacillin-tazobactam was administered via bladder catheterization for 7 days, yielding a favorable response characterized by symptom resolution and radiologic improvement. Microbiological assessment identified Escherichia coli and Klebsiella species as the causative pathogens, consistent with prior epidemiologic findings in emphysematous cystitis. The report underscores the utility of early CT imaging in non-specific presentations and reinforces that prompt administration of antimicrobial therapy, coupled with supportive measures such as bladder decompression, remains effective in immunosuppressed populations. [6]

References:

[1] Amano M, Shimizu T. Emphysematous cystitis: a review of the literature. Intern Med. 2014;53(2):79-82. doi:10.2169/internalmedicine.53.1121
[2] Thomas AA, Lane BR, Thomas AZ, Remer EM, Campbell SC, Shoskes DA. Emphysematous cystitis: a review of 135 cases. BJU Int. 2007;100(1):17-20. doi:10.1111/j.1464-410X.2007.06930.x
[3] Murata Y, Matsuo Y, Hiraoka E. Successful Conservative Management of Emphysematous Cystitis With Pneumoperitoneum: A Case Report and Literature Review. Cureus. 2023;15(8):e43769. Published 2023 Aug 19. doi:10.7759/cureus.43769
[4] Kim H, Park HC, Lee S, et al. Successfully treated Escherichia coli-induced emphysematous cyst infection with combination of intravenous antibiotics and intracystic antibiotics irrigation in a patient with autosomal dominant polycystic kidney disease. J Korean Med Sci. 2013;28(6):955-958. doi:10.3346/jkms.2013.28.6.955
[5] Kelesidis T, Osman S, Tsiodras S. Emphysematous cystitis in the absence of known risk factors: an unusual clinical entity. South Med J. 2009;102(9):942-946. doi:10.1097/SMJ.0b013e3181adf18c
[6] Sereno M, Gómez-Raposo C, Gutiérrez-Gutiérrez G, López-Gómez M, Casado E. Severe emphysematous cystitis: Outcome after seven days of antibiotics. Mcgill J Med. 2011 Jun;13(1):13. PMID: 22363178; PMCID: PMC3277337.

Literature Review

A search of the published medical literature revealed 4 studies investigating the researchable question:

What is the appropriate duration of treatment for emphysematous cystitis? Is there any evidence to support shorter courses of therapy?

Level of evidence

D - Case reports or unreliable data  Read more→



Please see Tables 1-4 for your response.


 

Successful Conservative Management of Emphysematous Cystitis With Pneumoperitoneum: A Case Report and Literature Review

Design

Case report

Case presentation

A 90-year-old woman was admitted to the hospital with a hemorrhagic gastric ulcer. A non-contrast CT scan initially showed no specific abnormalities. She was successfully treated with endoscopic hemostasis and vonoprazan fumarate. On the sixth day of hospitalization, she developed sudden lower abdominal pain and hematuria despite having an unremarkable medical history and no diabetes. Examination revealed pale appearance, acute distress, and mild tenderness in the lower abdomen but no rebound tenderness or muscular defense. Her lab results showed elevated leukocyte count and C-reactive protein, with gross hematuria. A subsequent contrast-enhanced CT scan detected gas within the bladder wall, indicative of emphysematous cystitis, and pneumoperitoneum, but no perforations.

Although surgical intervention was considered due to possible perforations, the patient's advanced age and malnutrition posed high surgical risks. Hence, conservative management was chosen. She was treated with a urethral catheter and intravenous meropenem. Clinical stability was achieved the next day, with fever and abdominal pain resolving. A urine culture showed Klebsiella pneumoniae, prompting a switch to ceftriaxone for two weeks. Follow-up CT imaging on day 18 showed resolution of emphysema in the bladder wall and no pneumoperitoneum. The patient remained stable and was transferred for chronic care and eventually discharged on day 40.

Study Author Conclusions

The report details a case involving an elderly, frail woman diagnosed with emphysematous cystitis accompanied by pneumoperitoneum. Due to her fragile health status, a conservative management approach was chosen instead of surgical intervention, which proved successful, allowing her to recover without surgery. Typically, pneumoperitoneum with emphysematous cystitis raises concerns about bladder perforation, often necessitating surgical intervention. However, there are instances, including this case, where conservative management has been effective.

A literature review was conducted to better understand such cases, analyzing reports from databases such as MEDLINE and Japana Centra Revuo Medicina Web. Fourteen cases between 2000 and 2023 were identified, inclusive of this one. Out of these, surgical exploration was performed in nine cases, revealing bladder perforation in four. Cases with bladder perforation generally presented with hemodynamic instability, while those without were stable and often managed conservatively. Despite these observations, hemodynamic stability alone isn't a reliable predictor for successful conservative management, as conditions like gastrointestinal perforation can still occur with stable vitals.

The report suggests that some patients with emphysematous cystitis and pneumoperitoneum might form a specific clinical subgroup that could be safely managed without surgery. The exact mechanism causing pneumoperitoneum without bladder perforation remains unclear, although hypotheses exist, such as bladder wall blebs bursting externally without a full transmural perforation. The report concludes by emphasizing the necessity of case accumulation and research to delineate which cases can be managed conservatively, as this could represent a significant advancement in managing similar clinical scenarios.

 

References:

Murata Y, Matsuo Y, Hiraoka E. Successful Conservative Management of Emphysematous Cystitis With Pneumoperitoneum: A Case Report and Literature Review. Cureus. 2023;15(8):e43769. Published 2023 Aug 19. doi:10.7759/cureus.43769

 

Successfully treated Escherichia coli-induced emphysematous cyst infection with combination of intravenous antibiotics and intracystic antibiotics irrigation in a patient with autosomal dominant polycystic kidney disease

Design

Case report

Case presentation

A 62-year-old female with autosomal dominant polycystic kidney disease (ADPKD) was admitted to a hospital for evaluation of intermittent fever, nausea, and left flank discomfort. She had a 15-year history of ADPKD, diagnosed alongside hypertension, and a family history with two brothers also affected. Despite previous episodes of recurrent cyst hemorrhage managed conservatively, her renal function had deteriorated, leading to hemodialysis since April 2011, with a daily urine output of approximately 200 cc. In the past, she was treated for a suspected cyst infection versus acute pyelonephritis with ciprofloxacin.

Recently, she experienced generalized weakness, anorexia, nausea, and persistent left flank discomfort, along with an intermittent fever. A CT scan revealed a large gas-forming cyst in the left kidney. Laboratory tests showed elevated white blood cell (WBC) counts and C-reactive protein (CRP) levels, with significant numbers of red blood cells (RBCs) and WBCs in the urinary sediment. Despite a week of intravenous ciprofloxacin therapy, her symptoms persisted.

Upon admission, physical examination indicated local tenderness in her left flank, although costovertebral angle tenderness was absent. Continued high levels of WBCs and CRP were observed. The decision was made to perform a percutaneous cystostomy drainage of the cyst, where aspiration of the cyst revealed high counts of WBCs and RBCs, with a culture confirming E. coli presence.

The treatment involved intravenous ciprofloxacin 400 mg daily for 1 week, followed by intracystic irrigation with a ciprofloxacin 100 mg (50 mL)and saline (450 mL). This regimen led to an improvement in symptoms and normalization of laboratory parameters. A follow-up CT scan showed a reduction in the size of the infected cyst from 8.1 cm to 4.7 cm. Following the intervention, the patient was discharged with a prescription for oral ciprofloxacin for an additional six weeks to ensure complete resolution.

Study Author Conclusions

Emphysematous urinary tract infections (UTIs) are uncommon but severe infections characterized by gas formation within the lower or upper urinary tract, often associated with necrotizing infection. These infections are more prevalent in individuals with diabetes, urinary tract obstructions, or those with weakened immune systems. Predominantly caused by E. coli and Klebsiella species, they typically require pathogenic bacterial strains capable of mixed acid fermentation and are exacerbated by hyperglycemia, ischemia, and local tissue necrosis.

Treatment strategies for emphysematous UTIs, particularly emphysematous pyelonephritis, depend on the infection's severity. Treatments often involve a combination of antibiotics and percutaneous cystostomy drainage or emergency nephrectomy. There are no definitive guidelines due to the infection's rarity. Fluoroquinolones are frequently used due to their effective intracystic penetration and bactericidal action against Gram-negative pathogens. Other antibiotics with good cyst penetration include chloramphenicol and metronidazole. However, antibiotic therapy alone is often insufficient due to poor cyst penetration, necessitating alternative approaches such as intracystic antibiotic irrigation.

Emphysematous cyst infections in autosomal dominant polycystic kidney disease (ADPKD) are notably challenging due to their life-threatening nature and lack of standardized treatment protocols. Only a few reported cases of emphysematous cyst infection exist, primarily occurring in end-stage ADPKD. The first successful treatment case of emphysematous cyst infection using a combination of intravenous antibiotics and intracystic antibiotic irrigation, instead of surgical nephrectomy, marks a meaningful therapeutic advancement. This approach may serve as a viable alternative for patients unable to withstand surgery or those not responding adequately to antibiotics alone. However, it requires careful consideration given the severity and poor prognosis associated with these infections.

 

References:

Kim H, Park HC, Lee S, et al. Successfully treated Escherichia coli-induced emphysematous cyst infection with combination of intravenous antibiotics and intracystic antibiotics irrigation in a patient with autosomal dominant polycystic kidney disease. J Korean Med Sci. 2013;28(6):955-958. doi:10.3346/jkms.2013.28.6.955

 

Emphysematous cystitis in the absence of known risk factors: an unusual clinical entity

Design

Case report

Case presentation

An 89-year-old woman presented to the hospital following a mechanical fall. Her significant medical history included chronic obstructive pulmonary disease, osteoarthritis, and hypertension. Despite being hemodynamically stable, she exhibited suprapubic tenderness, and laboratory tests revealed leukocytosis with high polymorphonuclear cells, alongside pyuria and bacteriuria. A computed tomography scan confirmed the presence of air in the bladder wall, indicative of emphysematous cystitis.

Initially treated with intravenous ciprofloxacin, she developed delirium, likely due to the drug. Due to a penicillin allergy, treatment was switched to intravenous aztreonam, which led to symptom improvement and a reduction in white cell count. She also experienced atrial fibrillation but ultimately recovered. After completing a 7-day antibiotic course, she was discharged to a rehabilitation facility. A follow-up abdominal x-ray a month later showed resolution of the bladder wall air, indicating recovery from the emphysematous cystitis.

Study Author Conclusions

Emphysematous cystitis is primarily diagnosed radiologically by detecting intramural gas within the urinary bladder wall, best visualized on abdominal imaging. While a plain abdominal x-ray can reveal curvilinear radiolucency marking the bladder wall, it lacks specificity. A computed tomography (CT) scan of the abdomen is more definitive, as it can detect air bubbles within the bladder lumen or wall, especially when symptoms obscure diagnosis. Magnetic resonance imaging (MRI) is not routinely used for this diagnosis due to insufficient evidence.

Laboratory findings often include pyuria and hematuria with a high rate of positive urine cultures, predominantly for Escherichia coli (57.4%) and Klebsiella pneumoniae (21.3%). Other associated organisms include Enterobacter aerogenes, Proteus mirabilis, Staphylococcus aureus, various streptococci, Clostridium perfringens, and Candida albicans, with occasional polymicrobial infections. Approximately half of the cases present with bacteremia.

Typically, emphysematous cystitis is managed medically with antibiotics and adequate bladder drainage, often through catheterization. In severe cases, bladder irrigation may be necessary if the patient cannot void or if blood clots are present. Surgical intervention is reserved for cases with complications such as urinary tract obstructions, stones, anatomical abnormalities, and emergencies like peritonitis, pneumoperitoneum, or perivesical abscesses.

The treatment duration averages 7-10 days based on clinical response, extended to 7 days in most instances to prevent complications and recurrence. Prognosis is generally positive, with most cases resolving within four days of therapy unless complicated by systemic dysfunction. Delayed diagnosis can result in severe consequences, including progression to overwhelming infection, ureteral or renal involvement, bladder rupture, or even death.

References:

Kelesidis T, Osman S, Tsiodras S. Emphysematous cystitis in the absence of known risk factors: an unusual clinical entity. South Med J. 2009;102(9):942-946. doi:10.1097/SMJ.0b013e3181adf18c

 

Severe emphysematous cystitis: Outcome after seven days of antibiotics

Design

Case report

Case presentation

A 70-year-old female patient with a history of diabetes and active chemotherapy for breast cancer, exhibited profound asthenia and pain in the right lower extremity without fever or urinary symptoms. Cross-sectional imaging through CT identified extensive gas accumulation within the bladder wall, confirming the presence of emphysematous cystitis.

Given the patient’s immunocompromised status, an empiric antimicrobial regimen was initiated alongside bladder catheterization, aiming to resolve the infection while preventing complications. Serial imaging demonstrated a marked reduction in intramural gas, suggesting clinical improvement with conservative treatment. A therapeutic course of IV piperacillin-tazobactam was administered via bladder catheterization for three weeks, yielding a favorable response characterized by symptom resolution and radiologic improvement after 7 days.

After three weeks of antibiotics, the patient's outcome was favorable with no evidence of relapse.

Study Author Conclusions

Emphysematous cystitis, while rare, is mainly seen in diabetic and immunocompromised patients. Appropriate treatment includes broad-spectrum antibiotics (e.g., penicillins, third-gen cephalosporins, fluoroquinolones); antifungal treatment may be warranted if a fungal pathogen is identified. Generally, antimicrobial therapy should be 3-6 weeks, depending on symptom improvement (e.g., gas production recovery).

In this case, microbiological assessment identified Escherichia coli and Klebsiella species as the causative pathogens, consistent with prior epidemiologic findings in emphysematous cystitis. The report underscores the utility of early CT imaging in non-specific presentations and reinforces that prompt administration of antimicrobial therapy, coupled with supportive measures such as bladder decompression, remains effective in immunosuppressed populations. 

 

References:

Sereno M, Gómez-Raposo C, Gutiérrez-Gutiérrez G, López-Gómez M, Casado E. Severe emphysematous cystitis: Outcome after seven days of antibiotics. Mcgill J Med. 2011;13(1):13.