What evidence is there surrounding long- and short-term outcomes for heart failure patients on midodrine?

Comment by InpharmD Researcher

The little evidence available on the use of midodrine in heart failure patients shows favorable short-term results when used as a bridge therapy to stabilize a patient's blood pressure in order to return to guideline-directed medical therapy. One study (presented as a poster abstract) found a significantly higher incidence of mortality in HFrEF patients taking midodrine; however, the groups were not even and midodrine users had a lower LVEF at baseline. Another retrospective study found HF patients discharged from the hospital on midodrine had a higher risk of 1-year mortality despite no difference in baseline severity of illness scores and reduced in-hospital mortality during the index visit. Most other data exists as case reports, some of which describe patients taking midodrine for years before tapering off and resuming GDMT.

Background

A 2023 review article provides a comprehensive summary of the existing literature on the use of midodrine in heart failure (HF) patients. While guideline-directed medical therapy (GDMT) plays a crucial role in managing heart failure, the potential for hypotension to hinder its initiation or up-titration is recognized. Midodrine demonstrates potential in addressing various causes of symptomatic hypotension, including vasovagal syncope, orthostatic hypotension in geriatric patients, neuro-cardiogenic syncope, autonomic nervous system dysfunction, and hypotension induced by hemodialysis. In advanced heart failure cases, a recent trial explored using midodrine to elevate blood pressure levels sufficiently for the prescription of disease-modifying therapies, but the approach remains somewhat contentious. The utilization of midodrine in HF has undergone multiple studies and investigations. The current evidence regarding the use of midodrine in HF is outlined in Table 1. [1]

Research indicates that midodrine can enhance blood pressure, diminish the necessity for vasopressor support, and facilitate GDMT prescription for patients who experience intolerance due to hypotension. However, concerns arise from reported increases in all-cause mortality in select studies, limited sample sizes, and the nonrandomized nature of certain study designs. To gain a comprehensive understanding of the risks and benefits associated with midodrine use in HF patients, additional investigations, including extensive randomized controlled trials and prolonged follow-up studies are warranted. Clinicians must carefully balance the potential benefits of midodrine in HF against the limited evidence and potential risks before considering its use. [1]

A 2021 retrospective cohort study evaluated the prevalence of midodrine prescription in hospitalized patients with decompensated heart failure with reduced ejection fraction (HFrEF) between January and December 2019, in which a total of 3,640 patients met inclusion criteria. Among included subjects, 9.3% (n= 340; mean left ventricular ejection fraction [LVEF] 25%) were prescribed midodrine as opposed to 90.7% (n= 3,330; mean LVEF 35%) who were not given midodrine. The results showed that all-cause mortality at 6 months from hospitalization was significantly higher in the midodrine group compared to those without (26.4% vs. 3.9%; p<0.001, relative risk [RR] 6.7, 95% confidence interval [CI] 5.2%-8.5%). Additionally, the patients on midodrine were more likely to be prescribed beta blockers, mineralocorticoid receptor antagonists (MRAs), and angiotensin receptor neprilysin inhibitors (ARNIs) when compared to those without (85% vs. 75%, 53% vs. 31%, 29% vs. 17%, respectively; p<0.001). The authors discuss the high prevalence of midodrine use in the systolic heart failure population, particularly in those with severely reduced LVEF likely due to treatment-induced hypotension, yet suggest a worse prognosis despite the adjustment for comorbidities and increased use of GDMT. Nonetheless, it should be noted that these findings are merely presented as a poster abstract, lacking further details on methodology and results, and the study specifically excluded diagnoses of end-stage renal disease, orthostatic hypotension, and LVEF > 50%. [2]

A prospective study, published in 2009, evaluated the effectiveness of midodrine in the optimization of heart failure therapy for patients encountering challenges due to pre-existing or treatment-induced hypotension. A total of 10 patients with heart failure due to systolic dysfunction and symptomatic hypotension hindering optimal therapy were enrolled. The exclusion criteria comprised severe valvular dysfunction, low heart rates (<40 beats per minute), liver failure, or patients undergoing hemodialysis. The study protocol involved initiating midodrine 5 mg PO every 6 hours, which was titrated up to a maximum of 10 mg every 6 hours. The patient’s blood pressure, B-type natriuretic peptide (BNP) levels, echocardiography, and medical therapy were closely monitored for 6 months. Background diuretic therapy was tailored based on individual volume status, and renal function was assessed using the Modification in Diet in Renal Disease formula. The results revealed notable improvements, with a higher percentage of patients achieving optimal heart failure therapy, supported by increased dosing percentages of ACE inhibitors/ARBs (20% vs. 57.5%; p<0.001), beta-blockers (37.5% vs. 75%; p<0.001), and spironolactone/eplerenone (43.7% vs. 95%; p<0.001). These adjustments corresponded with enhanced LVEF (baseline 24 ± 9.4 vs. 32.2 ± 9.9; p<0.001) and significant clinical improvements. The findings also revealed a major reduction in total hospital admissions (32 vs.12; p= 0.02) and total hospital days (150 vs. 58; p= 0.02) following midodrine treatment. Moreover, patients experienced improved blood pressure, functional class, reduced BNP levels, decreased left ventricular end-diastolic diameter (LVEDD), and increased LVEF at the six-month mark. It was also noted that midodrine was well tolerated among the included patients, with no reported side effects. However, experiences from non-study patients with concurrent benign prostatic hypertrophy occasionally developed prostatism, which was mitigated by adjusting the midodrine dosage. Based on these findings, it was concluded that midodrine was well-tolerated and aided in the up-titration of neurohormonal-blocking agents, resulting in reverse remodeling and enhanced clinical outcomes. However, due to the small cohort size, larger-scale investigations are needed to further validate these findings. [3]

A 2006 prospective study evaluated 10 consecutive patients with HF due to systolic dysfunction and symptomatic hypotension interfering with optimal medical therapy. Patients began midodrine at 5 mg orally every 6 hours, with the option to escalate to a maximum of 10 mg every 6 hours. Systolic blood pressure (SBP) rose from a baseline of 79.2 ± 4.6 to 99.0 ± 11 mmHg (p <0.0004), while BNP decreased from 1402 ± 1559 to 706 ± 592 (p <0.0001). NYHA class was reduced from 3.5 to 2.4 at six months. The utilization of ACE inhibitors/ARBs increased from 54 to 81%, beta-blockers from 82 to 100%, and spironolactone/eplerenone from 72.7 to 91% of the optimal dose. LVEF improved from a baseline of 24 ± 9.44 to 32.2 ± 9.9 % (p<0.001), and LVEDD decreased from a baseline of 6.2 cm to 5.9 cm (p = 0.04). It was suggested that the use of midodrine is safe in patients with heart failure due to systolic dysfunction with hypotension despite concerns regarding vasoconstriction. Additionally, it allowed patients to receive optimal medical therapy with neurohormonal antagonists leading to significant improvements in reverse modeling manifested by increases in LVEF, reduction in LVEDD, and improved outcomes. It should be noted that these results were only presented as an abstract and may not be comprehensive. [4]

Two case reports describe the feasibility of midodrine use in patients with HFrEF and hypotension. Case 1 presents an 81-year-old female with a number of comorbidities being repeatedly admitted for the exacerbation of right-sided heart failure and associated hypotension. Despite optimized intravenous (IV) noradrenaline infusion and diuretic therapy, she required hemofiltration sessions due to deteriorated kidney function. Following 21 days of efforts to wean the patient off of IV noradrenaline, midodrine was initiated, starting 5 mg TID on off-dialysis and 7.5 mg TID on dialysis days. IV support was successfully weaned off and completely discontinued after an increased dose of midodrine 10 mg TID both on- and off-dialysis days. No major adverse events (AEs) were noted during the treatment, and subsequent hemodialysis was performed without the need for further IV support. Case 2 presents a 79-year-old male patient, frequently admitted due to symptoms of heart failure and hypotension, which limit optimal drug titration and initiation of GDMT for class 1 heart failure. The patient’s blood pressure remained low with deterioration of renal function and volume overload despite both IV inotropic (dobutamine and levosimendan) and vasopressor (noradrenaline) support. Hemofiltration was initiated, and in an attempt to wean the patient off IV noradrenaline and possible initiation of GDMT, oral midodrine 2.5 mg TID was started, with a gradual dose increase to 10 mg TID. Subsequently, the patient was successfully weaned off over 3 weeks, tolerated hemodialysis sessions without the need for IV support, and started on small, gradual doses of GDMT administration. The authors acknowledge the struggles with proper initiation and up-titration of GDMT for class I indication in patients with HFrEF due to hypotension. The authors suggest that midodrine may be used off-label to help wean hypotensive patients off of IV vasopressors and allow initiation and possible up-titration of GDMT. [5]

References:

[1] Gautam S, Lamichhane S, Sharma NR, et al. Use of midodrine in heart failure: a review. Ann Med Surg (Lond). 2023;85(6):2808-2813. Published 2023 May 24. doi:10.1097/MS9.0000000000000922
[2] Scoma C, Dae-Hyun L, Cohen A, Fernandez J. Prevalence of midodrine use in patients admitted with systolic congestive heart. J Am Coll Cardiol. 2021;77(18):678. doi: 10.1016/S0735-1097(21)02037-4.
[3] Zakir RM, Folefack A, Saric M, Berkowitz RL. The use of midodrine in patients with advanced heart failure. Congest Heart Fail. 2009;15(3):108-111. doi:10.1111/j.1751-7133.2008.00042.x
[4] Folefack A, Zakir RM, Saric M, Berkowitz RL. Midodrine increases blood pressure in hypotensive heart failure patients facilitating optimization of heart failure therapy leading to improved outcomes. J Cardiac Fail. 2006;12(6):S129. doi: 10.1016/j.cardfail.2006.06.448.
[5] Hajjiah A, Maadarani O, Bitar Z, et al. Use of Midodrine in Heart Failure: Two Case Reports and a Review of the Literature. Eur J Case Rep Intern Med. 2022;9(3):003246. Published 2022 Mar 18. doi:10.12890/2022_003246

Literature Review

A search of the published medical literature revealed 2 studies investigating the researchable question:

Patient with HFrEF and orthostatic hypotension. All GDMT is on hold. Can midodrine be used safely?

Please see Tables 1-2 for your response.


 

Summary of the current evidence regarding using of midodrine in heart failure
Paper title Journal References Number of participants Findings
Midodrine As a Bridge to Enable Use of Life Enhancing Therapies in Chronic Heart Failure. Journal of Cardiac Failure, 2020 Krishnaswami v., Desiree L., Teressa M. et. al 60 After starting midodrine, 94% of the patients who were intolerant to BB, ACE/ARB and ANRI could tolerate BB (mostly carvedilol) or ARNI or MRA (P<0.001). The mean improvement in SBP was 8 mm Hg, ±4 mm Hg).
Continuation of Newly Initiated Midodrine Therapy After Intensive Care and Hospital Discharge: A Single-Center Retrospective Study Critical Care Medicine, 2019 .Rizvi, Mahrukh S., Nei, Andrea M., Gajic, Ognjen, Mara, Kristin C., Barreto, Erin F 1010 Discharge from the ICU on midodrine was associated with a significantly shorter ICU length of stay (7.5±8.9 vs. 10.6±13.4 days) and reduced risk of in-hospital mortality (hazard ratio, 0.47 [95% CI, 0.32-0.70]; P<0.001), despite no difference in baseline severity of illness scores. In contrast, patients discharged from the hospital on midodrine had a higher risk of 1-year mortality (hazard ratio, 1.60 [95% CI, 1.26–2.04]; P<0.001).
Prevalence of midodrine use in patients admitted with systolic congestive heart failure Journal of American college of Cardiology, 2021 Christopher Scoma, Dae Hyun Lee, Adam Cohen, and Joel Fernandez 3640 All-cause mortality at 6 months from hospitalization was significantly higher in the midodrine group compared to those without midodrine (26.4% vs. 3.9%; P<0.001, RR 6.7, 95% CI 5.2%–8.5%).
The use of midodrine in patients with advanced heart failure Congestive Heart Failure, 2009 R. Zakir, A. Folefack, M. Saric, R. Berkowitz 10 With Midodrine therapy, SBP increased from a baseline of 79.2±4.6 to 99.0±11 mmHg (P<0.0004), BNP decreased from 1402±1559 to 706±592 (P<0.0001), and NYHA Class decreased from 3.5 to 2.4 at 6 months. This led to an improvement in left ventricular ejection fraction (baseline 24±9.4 vs. 32.2±9.9; P<0.001), LVEDD decreased from baseline of 6.2 cm to 5.9 cm (P=0.04) and clinical outcomes, with a significant reduction in total hospital admissions (32 vs. 12; P=0.02) and total hospital days (150 vs. 58; P=0.02).
Hemodialysis in Hypotensive heart failure using midodrine Am J Med Sci , 2009 Suzzane M. Bergman 5 While receiving midodrine, each of the five patients on midodrine had less hypotension as measured by the MAP of the lowest blood pressures recorded during dialysis (P<0.03).
Midodrine to optimize heart failure therapy in patients with concurrent hypotension SAGE Open Medical Case Reports, 2022 Paul Shiu, G. S. Grewal, T. Kozik 4 Exacerbations of heart failure with reduced ejection fraction may be ameliorated with outpatient midodrine titration among patients with baseline persistent hypotension.
Use of Midodrine in Heart Failure: Two Case Reports and a Review of the Literature European Journal of Case Reports in Internal Medicine, 2022 Adnan Hajjiah, O. Maadarani, Z. Bitar, Boutros Hanna, R. Elshabasy, M. Abdelfatah, Mohammad Gohar 2 Midodrine may be used off-label in patients with heart failure with reduced ejection fraction and symptomatic hypotension to allow optimization of medical therapy.

 

References:

Adapted from:
Gautam S, Lamichhane S, Sharma NR, et al. Use of midodrine in heart failure: a review. Ann Med Surg (Lond). 2023;85(6):2808-2813. Published 2023 May 24. doi:10.1097/MS9.0000000000000922

 

Midodrine to Optimize Heart Failure Therapy in Patients with Concurrent Hypotension

Design

Case series

Case presentation

A 56-year-old male Caucasian complained of feeling lightheaded and dizzy when he arrived at the hospital. He had a history of hypothyroidism, dyslipidemia, hypertension, and chronic systolic heart failure. An echocardiography revealed a moderately dilated left ventricle and a left ventricular ejection fraction (LVEF) of 35%. Once an electrophysiologist consultation was obtained, an implanted dual-chamber internal cardiac defibrillator (ICD) was made. Moreover, a heart catheterization revealed no evidence of atherosclerotic illness.

At the time of release, he was able to take carvedilol 3.125 mg twice a day plus ramipril 2.5 mg daily. His LVEF had improved to 40% on an office echocardiography. After three years of close monitoring by the cardiologist, he experienced symptoms of hypotension (70/52 mmHg). After stopping his ramipril, the patient experienced episodes of hypotension again, so three months later, his carvedilol and losartan were also stopped. 

At that point, the patient's blood pressure and symptoms stabilized, but a week later, he started experiencing frequent dizziness with a corresponding blood pressure of 90/60 mmHg. Midodrine 2.5 mg twice daily was initiated, with a graduate titration to TID (or QID PRN; max 10 mg/day). Two years later, he was continued on midodrine daily (dose unspecified).

After several months, his LVEF improved to 43%; therefore, losartan 25 mg daily was reinstated. Eventually, the carvedilol was increased to 6.25 mg BID. Weaning off of midodrine occurred after several months of continuing use, and a follow-up echocardiography showed an LVEF of 52%. Before stopping, the 10 mg TID taper regimen was tapered down gradually to 5 mg TID, then to BID, and then to daily. With an ejection fraction (EF) of roughly 58%, the patient still took his cardiac medications as prescribed at publication. All things considered, this patient's LVEF improved overall after taking midodrine for around 24 months and starting GDMT again.

Case 2

A 58-year-old African American woman with ventricular fibrillation had effective defibrillation without experiencing any neurological complications. Her medical history included obesity and hypertension but no cardiac history. After a cardiac catheterization, which was performed after her ECG revealed a left bundle branch block, it was discovered that she had an EF of 18% but no major coronary artery disease. The patient received an implanted ICD/cardiac resynchronization therapy device prior to being sent home on furosemide, carvedilol, and losartan.

Two weeks later, she was readmitted to the hospital because of hypotension, and her losartan and carvedilol were stopped. Following discharge, the patient was put on 2.5 mg of midodrine BID, then the dosage was increased to 5 mg TID after going from 2.5 mg TID.

Gradually, the physicians resumed her carvedilol and losartan, titrating them up as she continued taking her diuretic. The midodrine was weaned off at her 5 mg TID dose without a taper after about two months. At a follow-up appointment, an echocardiography revealed that her left ventricular ejection fraction had risen to 28%. After two years, when she was stable, doctors started her on sacubitril-valsartan and stopped her losartan.

She was taking carvedilol 25 mg BID, sacubitril-valsartan 49/51 mg BID, and furosemide 40 mg as needed at the time of publishing. She was employed full-time, and her most recent EF on this pharmaceutical regimen was 53% with no signs of heart failure. In conclusion, the patient's LVEF significantly increased over time, and she was able to resume her GDMT for heart failure after two months of midodrine medication.

Case 3

A 61-year-old Caucasian woman with a history of hypertension was seen at a cardiology clinic, and a screening ECG revealed that she had a sinus rhythm with a left bundle branch block. Her nuclear scan revealed no evidence of myocardial ischemia, and her echocardiography revealed that her LVEF was 48%. She arrived at the emergency room eight years later with low blood pressure brought on by several submassive pulmonary emboli. She was admitted with an echocardiography revealing a 30% LVEF and persistent atrial fibrillation, for which amiodarone was prescribed. Her chest x-ray during her hospital stay showed radiographic signs of congestive heart failure, and her low blood pressure necessitated the use of an intravenous vasopressor.

After a few days, the doctors began her on 2.5 mg of midodrine BID and gradually increased her dosage to 5 mg of TID, after which they were able to wean her off the vasopressor. She was unable to tolerate the small doses of carvedilol that they sought to start her on concurrently. Following one week, she was released from the hospital with apixaban, losartan 25 mg daily, metoprolol succinate 25 mg daily, midodrine 5 mg TID, and spironolactone 25 mg daily. They switched her losartan to sacubitril-valsartan 24/26 BID at her follow-up visit a week later. Clinicians were able to stop administering midodrine at 5 mg TID after a month without her heart failure symptoms getting worse. An EF of 40% and normal coronaries were found during her most recent cardiac catheterization at the time of publication.

Case 4

A 57-year-old Hispanic woman with a history of chronic systolic heart failure and a left ventricular ejection fraction of 58% arrived at the hospital with acute, chronic systolic heart failure brought on by a myocardial infarction that showed non-ST-segment elevation. Her medical history also included hypertension, dyslipidemia, insulin-independent diabetes, and tobacco use disorder. Upon cardiac catheterization, the patient revealed moderate to severe aortic regurgitation along with a 5-centimeter aneurysm affecting the ascending and abdominal aorta. Her electrocardiogram just before discharge revealed a slight LV hypokinesis, an LVEF of 31%, and a mechanical aortic valve operating normally. The patient had an abdominal aortic aneurysm repaired a few weeks later.

The patient experienced numerous hospital admissions for heart failure and inadequate blood sugar management during the course of the next two years. Her low blood pressure made it challenging to treat her heart failure with GDMT. Before starting carvedilol 6.25 mg, sacubitril-valsartan 25/26 twice daily, spironolactone 25 mg daily, and carvedilol 6.25 mg, clinicians started midodrine at 5 mg BID and increased to TID dosage.

As her heart condition improved over the course of the following year, they were able to wean her off of the 5 mg TID of midodrine and transition to a once-daily dosage before stopping it altogether. Her most recent LVEF was 49%, and in the six months before publication, she had no more hospital hospitalizations for heart failure. 

Study Author Conclusions

This paper presented several cases using midodrine, a medication that has been used for over 20 years for orthostatic hypotension to improve GDMT in heart failure patients with refractory hypotension. The authors advocate its use in non-ischemic heart failure patients to maintain a conservative systolic BP >100 mm Hg. Upon LV function and EF improvement, midodrine should be appropriately be tapered to discontinuation. In this way, midodrine helps bridge to resuption of GDMT.

 

References:

Shiu P, Grewal GS, Kozik TM. Midodrine to optimize heart failure therapy in patients with concurrent hypotension. SAGE Open Med Case Rep. 2022;10:2050313X221100400. Published 2022 May 18. doi:10.1177/2050313X221100400